Clinical and imaging findings of klippel-trenaunay syndrome: A case report

Anandhika Dwijaya; Muhammad Hidayat Surya Atmaja

doi:10.21744/ijhms.v5n1.1860

Authors

Anandhika Dwijaya Radiology residency, Department of Radiology, Dr Soetomo General Academic Hospital, Faculty of Medicine, Universitas Airlangga, Surabaya, Indonesia
Muhammad Hidayat Surya Atmaja
hidayatsuryaatmaja@gmail.com
Staff of Radiology Department, Dr Soetomo General Academic Hospital, Faculty of Medicine, Universitas Airlangga, Surabaya, Indonesia

Keywords:

arteriography, imaging, intervention, klippel-trenaunay syndrome, MRI

Abstract

Klippel-Trenaunay syndrome (KTS) is characterized by the classic triad of capillary malformations manifesting as a "port-wine stain", venous varicosities, and bone and/or soft tissue hypertrophy. Imaging could help to diagnose and evaluation of KTS. Case Presentation: We report a 12-year-old with progressive enlargement of the right lower limb with geographic stain and venous varicosities. The patient also underwent MRI and angiography, which revealed multiple nidus with multiple feeding arteries. Conclusion: Klippel-Trenaunay Syndrome is a rare condtion. MRI and Arteriography could help diagnose KTS for confirmation, monitoring progression, or identification of complications.

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